{"id":2046,"date":"2022-09-22T17:12:31","date_gmt":"2022-09-22T08:12:31","guid":{"rendered":"https:\/\/www.jichi.ac.jp\/alle\/cms\/?p=2046"},"modified":"2022-10-20T09:05:29","modified_gmt":"2022-10-20T00:05:29","slug":"%e6%8a%84%e8%aa%ad%e4%bc%9a%e3%80%802022%e5%b9%b49%e6%9c%8822%e6%97%a5","status":"publish","type":"post","link":"https:\/\/www.jichi.ac.jp\/alle\/reading-session\/%e6%8a%84%e8%aa%ad%e4%bc%9a%e3%80%802022%e5%b9%b49%e6%9c%8822%e6%97%a5\/","title":{"rendered":"\u6284\u8aad\u4f1a\u30002022\u5e749\u670822\u65e5"},"content":{"rendered":"<p><span style=\"font-size: 11pt;\">\u81ea\u6cbb\u533b\u79d1\u5927\u5b66\u30a2\u30ec\u30eb\u30ae\u30fc\u81a0\u539f\u75c5\u5b66\u3067\u306f\u6bce\u9031\u533b\u5c40\u54e1\u304c\u4ea4\u4ee3\u3067\u6284\u8aad\u4f1a\u3092\u884c\u3063\u3066\u304a\u308a\u307e\u3059\u3002<\/span><\/p>\n<h1><span style=\"font-family: verdana, geneva, sans-serif; font-size: 11pt; color: #000080;\">Therapeutic options in VEXAS syndrome: insights from a retrospective series<\/span><\/h1>\n<p><span style=\"font-family: verdana, geneva, sans-serif; font-size: 11pt; color: #000080;\">Estelle Bourbon<sup>\u00a0<\/sup>,\u00a0Ma\u00ebl Heiblig<sup>\u00a0<\/sup>,\u00a0Mathieu Gerfaud Valentin<sup>\u00a0<\/sup>,\u00a0Thomas Barba<sup>\u00a0<\/sup>,\u00a0C\u00e9cile-Audrey Durel<sup>\u00a0<\/sup>,\u00a0Jean Christophe Lega<sup>\u00a0<\/sup>,\u00a0Fiorenza Barraco<sup>\u00a0<\/sup>,\u00a0Pascal S\u00e8ve<sup>\u00a0<\/sup>,\u00a0Yvan Jamilloux<sup>\u00a0<\/sup>,\u00a0Pierre Sujobert<sup>\u00a0<\/sup><\/span><\/p>\n<p><span style=\"font-family: verdana, geneva, sans-serif; font-size: 11pt; color: #000080;\">Blood.\u00a02021 Jul 1;137(26):3682-3684.\u00a0doi: 10.1182\/blood.2020010177.<\/span><\/p>\n<p><span style=\"font-family: verdana, geneva, sans-serif; font-size: 11pt; color: #000080;\">VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflam- matory, somatic)\u306f\u518d\u767a\u6027\u591a\u767a\u8edf\u9aa8\u708e\u3001\u9aa8\u9ac4\u7570\u5f62\u6210\u75c7\u5019\u7fa4\u306a\u3069\u306e\u8840\u6db2\u75be\u60a3\u3001Sweet\u75c5\u306a\u3069\u3092\u8868\u73fe\u7cfb\u3068\u3059\u308b\u75be\u60a3\u3067\u3042\u308a\u3001E1-\u30e6\u30d3\u30ad\u30c1\u30f3\u30ea\u30ac\u30fc\u30bc(UBA1)\u306b\u4f53\u7d30\u80de\u7a81\u7136\u5909\u7570\u304c\u898b\u3089\u308c\u308b\u3053\u3068\u304c\u77e5\u3089\u308c\u3066\u3044\u307e\u3059\u3002\u65b0\u3057\u3044\u75be\u60a3\u6982\u5ff5\u306e\u75c7\u5019\u7fa4\u3067\u3042\u308a\u3001\u78ba\u7acb\u3055\u308c\u305f\u6cbb\u7642\u6cd5\u306f\u307e\u3060\u3042\u308a\u307e\u305b\u3093\u3002\u672c\u8ad6\u6587\u3067\u306f\u3001\u518d\u767a\u6027\u591a\u767a\u8edf\u9aa8\u708e\u3001\u9aa8\u9ac4\u7570\u5f62\u6210\u75c7\u5019\u7fa4\u3001Sweet\u75c5\u306a\u3069\u3068\u8a3a\u65ad\u3055\u308c\u305fVEXAS syndrome \u3068\u8003\u3048\u3089\u308c\u308b19\u4f8b\u306e\u7537\u6027\u75c7\u4f8b\u3092\u89e3\u6790\u3057\u305f\u5831\u544a\u3067\u3001\u5b9f\u969b\u306bUBA1\u907a\u4f1d\u5b50\u306b\u5909\u7570\u306e\u898b\u3089\u308c\u305f\u75c7\u4f8b\u306f11\u4f8b\u3067\u3057\u305f\u3002PSL\u3001MTX\u3001\u6297TNF\u963b\u5bb3\u85ac\u3001\u6297IL-6\u53d7\u5bb9\u4f53\u6297\u4f53\u3001\u30b7\u30af\u30ed\u30b9\u30dd\u30ea\u30f3\u306a\u3069\u3092\u6cbb\u7642\u85ac\u3068\u3057\u3066\u7528\u3044\u3089\u308c\u3066\u3044\u307e\u3059\u304c\u3053\u308c\u3089\u306e\u85ac\u5264\u7d99\u7d9a\u7387\u306f\u4f4e\u304f\u3001\u65e9\u671f\u306b\u4e2d\u6b62\u3055\u308c\u3066\u3044\u307e\u3057\u305f\u3002\u73fe\u6bb5\u968e\u3067\u3001\u75c7\u4f8b\u6570\u304c\u5c11\u306a\u3044\u3053\u3068\u3084\u30d5\u30a9\u30ed\u30fc\u671f\u9593\u304c\u77ed\u3044\u3053\u3068\u304b\u3089\u78ba\u5b9a\u7684\u306a\u7d50\u8ad6\u306f\u5c0e\u304d\u51fa\u305b\u307e\u305b\u3093\u304c\u3001JAK\u963b\u5bb3\u85ac\u306f\u7d99\u7d9a\u3067\u304d\u3066\u304a\u308a\u3001\u4eca\u5f8c\u52b9\u679c\u3092\u671f\u5f85\u3057\u305f\u3044\u85ac\u5264\u3068\u3057\u3066\u6319\u3052\u3089\u308c\u307e\u3057\u305f\u3002<\/span><\/p>\n<p style=\"text-align: right;\"><span style=\"font-size: 11pt; color: #000080;\">\u62c5\u5f53\u3000N<\/span><\/p>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"\u81ea\u6cbb\u533b\u79d1\u5927\u5b66\u30a2\u30ec\u30eb\u30ae\u30fc\u81a0\u539f\u75c5\u5b66\u3067\u306f\u6bce\u9031\u533b\u5c40\u54e1\u304c\u4ea4\u4ee3\u3067\u6284\u8aad\u4f1a\u3092\u884c\u3063\u3066\u304a\u308a\u307e\u3059\u3002 Therapeutic options in VEXAS syndrome: insights from a retrospective se &#8230;","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[7],"tags":[],"class_list":["post-2046","post","type-post","status-publish","format-standard","hentry","category-reading-session"],"_links":{"self":[{"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/posts\/2046","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/comments?post=2046"}],"version-history":[{"count":4,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/posts\/2046\/revisions"}],"predecessor-version":[{"id":2050,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/posts\/2046\/revisions\/2050"}],"wp:attachment":[{"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/media?parent=2046"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/categories?post=2046"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.jichi.ac.jp\/alle\/wp-json\/wp\/v2\/tags?post=2046"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}